Cardiol Young
. 2026 Jan 14:1-3.
doi: 10.1017/S1047951125110706. Online ahead of print. https://pubmed.ncbi.nlm.nih.gov/41530898/
The first reported coexistence of hepatopulmonary fusion and surgically palliated hypoplastic left heart syndrome
Mollie Westrick 1, Jennifer Mansour 1, Subhadra Shashidharan 1 2, Matthew S Clifton 1 2, Megan M Durham 1 2, Fred H Rodriguez Iii 1 3
Affiliations Expand
- PMID: 41530898
- DOI: 10.1017/S1047951125110706
Abstract
Hepatopulmonary fusion is a rare defect describing the physical connection of liver and lung. A neonate with hypoplastic left heart syndrome arrived at the hospital with concern for congenital diaphragmatic hernia, later found to have hepatopulmonary fusion. In the coming months, he underwent a series of operations, including ligation of the hepatopulmonary fusion and the first two stages of surgical palliation of hypoplastic left heart syndrome. He ultimately died of septic shock at 15 months of age.
Keywords: congenital diaphragmatic hernia; hepatopulmonary fusion; hypoplastic left heart syndrome.
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