Research: Acute Budd-Chiari syndrome caused by inferior vena cava compression from a congenital diaphragmatic hernia.

Ann R Coll Surg Engl. 2020 Jun 15:e1-e3. doi: 10.1308/rcsann.2020.0106. [Epub ahead of print] https://pmlegacy.ncbi.nlm.nih.gov/pubmed/32538105

Acute Budd-Chiari syndrome caused by inferior vena cava compression from a congenital diaphragmatic hernia.

Wcislo KM1,2Hall CE1,2Abbassi-Ghadi N3.

Author information

Abstract

Acute Budd-Chiari syndrome is a rare condition characterised by obstruction of hepatic venous outflow. We describe the case of a 52-year-old man, with a congenital Morgagni diaphragmatic hernia, who presented with acute onset abdominal pain, shortness of breath, lactic acidosis, hyperbilirubinaemia and transaminasaemia. Computed tomography revealed strangulation of the diaphragmatic hernia and extrinsic compression of the inferior vena cava from the herniated viscera. Emergency surgery was carried out to repair the hernia with a biosynthetic mesh, with complete resolution of the Budd-Chiari syndrome.

KEYWORDS:

Acute Budd–Chiari syndrome; Gastroenterothorax; Inferior vena cava compression; Morgagni herniaPMID: 32538105 DOI: 10.1308/rcsann.2020.0106

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