JACC Case Rep

. 2022 May 18;4(10):596-603. doi: 10.1016/j.jaccas.2022.03.027. https://pubmed.ncbi.nlm.nih.gov/35615212/

Multimodality Approach to a Complex Scimitar Syndrome: How Advanced Diagnostics Can Guide Therapeutic Strategies

Alberto Clemente ¹, Gaia Viganò ², Luigi Festa ³, Ettore Remoli ¹, Chiara Marrone ³, Duccio Federici ², Vitali Pak ², Dante Chiappino ¹, Giuseppe Santoro ³, Lamia Ait-Ali ⁴Affiliations expand

• PMID: 35615212
• PMCID: PMC9125519
• DOI: 10.1016/j.jaccas.2022.03.027

Free PMC article

Abstract

We report an unusual association of scimitar syndrome with right diaphragmatic hernia, left-sided aortic arch with “aberrant right subclavian artery” in a 2-year-old boy who underwent stepwise transcatheter occlusion of a significant aortopulmonary collateral followed by surgical treatment for the repair of the diaphragmatic hernia and esophageal compression. (Level of Difficulty: Advanced.).

Keywords: APC, aortopulmonary collateral; ARSA, aberrant right subclavian artery; CCT, cardiac computed tomography; CDH, congenital diaphragmatic hernia; CMR, cardiac magnetic resonance; HPF, hepatopulmonary fusion; SS, scimitar syndrome; aberrant right subclavian artery; anomalous pulmonary venous return; congenital heart disease; diaphragmatic hernia; scimitar syndrome.

© 2022 The Authors.