Int J Surg Case Rep
. 2024 Sep 24:124:110331.
doi: 10.1016/j.ijscr.2024.110331. Online ahead of print. https://pubmed.ncbi.nlm.nih.gov/39326375/
A unique case of hepatopulmonary fusion in congenital diaphragmatic hernia causing pulmonary hypoplasia in a newborn: A case report study
Kamar Shaker 1, Khaled Alomar 2, Youssef Chouman 3, Alhasan Rastanawi 3, Mohammed Abd Alkader 4, Nader Eid 5
Affiliations Expand
- PMID: 39326375
- DOI: 10.1016/j.ijscr.2024.110331
Free article
Abstract
Introduction and significance: Hepatopulmonary fusion is a rare congenital malformation associated with right-sided diaphragmatic hernia. Often diagnosed during surgery, it carries a high mortality rate.
Case presentation: We present a case of a full-term infant who exhibited shortness of breath from birth. Radiological examinations confirmed a right congenital diaphragmatic hernia, and subsequent surgery revealed hepatopulmonary fusion.
Clinical discussion: While hepatopulmonary fusion is uncommon, it should be considered in the differential diagnosis of right-sided congenital diaphragmatic hernia (CDH). Preoperative evaluation for vascular malformations and meticulous surgical planning are essential.
Conclusion: Managing hepatopulmonary fusion poses significant challenges for surgeons. Its association with pulmonary malformations increases surgical complexity, risk, and adversely impacts prognosis, as exemplified in our case.
Keywords: Bochdalek; Case report; Fusion; Hepatopulmonary; Pulmonary hypoplasia.
Copyright © 2024 The Authors. Published by Elsevier Ltd.. All rights reserved.
